头颈部腺泡状软组织肉瘤临床研究进展

摘要/Abstract

摘要： 腺泡状软组织肉瘤（alveolar soft part sarcoma，ASPS）是一类较罕见的软组织恶性肿瘤，主要表现为缓慢生长的无痛性肿块，通常情况下难以早期确诊，且极易出现远处转移，因此预后不佳。近年来，随着病例数的不断积累，以及相关技术水平的发展，ASPS的诊治方法不断得以提高和完善。本文对相关文献进行总结，从诊断、治疗及预后等方面对头颈部ASPS的研究进展做一综述。

关键词: 腺泡状软组织肉瘤, 头颈部, 肉瘤

Abstract: Alveolar soft part sarcoma (ASPS) is an extremely rare malignant neoplasm that accounts for less than 1% of all soft tissue sarcomas. Despite being a slow-growing tumor with an asymptomatic course, ASPS demonstrates a disproportionate frequency of distant metastases even at the early stages of disease. The delay of diagnosis brings about many difficulties to obtain a more favorable clinical course. Recently, owing to the development of technique, the diagnosis and treatment progress of ASPS continue to improve. This paper summarized the literatures on diagnosis, treatment progress and prognosis of ASPS of the head and neck region.

Key words: Alveolar soft part sarcoma, Head and neck region, Sarcoma

中图分类号:

R739.8

王宏伟, 王绪凯, 秦兴军, 张陈平. 头颈部腺泡状软组织肉瘤临床研究进展[J]. 中国口腔颌面外科杂志, 2016, 14(3): 276-281.

WANG Hong-wei, WANG Xu-kai, QIN Xing-jun, ZHANG Chen-ping. Diagnosis, treatment and prognosis of alveolar soft part sarcoma of the head and neck region[J]. China J Oral Maxillofac Surg, 2016, 14(3): 276-281.

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