口腔颌面部恶性外周神经鞘膜瘤: 1例报告及文献复习

中国口腔颌面外科杂志 ›› 2014, Vol. 12 ›› Issue (1): 91-94.

口腔颌面部恶性外周神经鞘膜瘤: 1例报告及文献复习

董瑞^{1, 2, *}, 陶冶^{1, *}, 胡敏¹, 陈鹏¹, 王高飞¹, 令狐大科¹

1.解放军总医院口腔颌面外科,北京 100853; 2.天津医科大学口腔医院口腔颌面外科,天津 300070

收稿日期:2013-07-03 修回日期:2013-08-08 出版日期:2014-02-10 发布日期:2014-02-10
通讯作者: 胡敏,Tel：010-66938316,E-mail: humin48@vip.163.com
作者简介:董瑞（1982-）,男,硕士,住院医师,E-mail：alexdong99@gmail.com,现在天津医科大学口腔医院工作；陶冶（1983-）,男,学士,住院医师,E-mail：424515@qq.com。*并列第一作者

Malignant peripheral nerve sheath tumors of the oral and maxillofacial region: report of a case and review of the literature

DONG Rui^{1, 2}, TAO Ye¹, HU Min¹, CHEN Peng¹, WANG Gao-fei¹, LINGHU Da-ke¹

1.Department of Oral and Maxillofacial Surgery, The General Hospital of People’s Liberation Army. Beijing 100853; 2.Department of Oral and Maxillofacial Surgery, Stomatology hospital of Tianjin Medical University. Tianjin 300070, China

Received:2013-07-03 Revised:2013-08-08 Online:2014-02-10 Published:2014-02-10

摘要/Abstract

摘要： 恶性外周神经鞘膜瘤(MPNST)是一种较为少见的恶性肿瘤,头颈部尤为少见。本文报告1例口腔颌面部MPNST患者,并结合国内外相关文献,探讨其临床表现、组织病理学及影像学特点、治疗及预后。MPNST是一种恶性程度较高的恶性肿瘤,手术治疗复发率较高,局部复发和远处转移是导致死亡的主要原因。

关键词: 外周神经鞘瘤, 恶性外周神经鞘膜瘤, 口腔颌面部

Abstract: Malignant peripheral nerve sheath tumor (MPNST) is a rare malignant tumor, even in the head and neck areas. This article reported a case of MPNST in oral and maxillofacial region, and discussed the clinical manifestation of MPNST, histopathological and imaging features, treatment and prognosis with related literature review. MPNST is a kind of high malignant tumor, recurrence rate after surgery is high, local recurrence and distant metastasis is the main cause of death.

Key words: Peripheral nerve sheath tumor, Malignant peripheral nerve sheath tumor, Oral and maxillofacial region

董瑞, 陶冶, 胡敏, 陈鹏, 王高飞, 令狐大科. 口腔颌面部恶性外周神经鞘膜瘤: 1例报告及文献复习[J]. 中国口腔颌面外科杂志, 2014, 12(1): 91-94.

DONG Rui, TAO Ye, HU Min, CHEN Peng, WANG Gao-fei, LINGHU Da-ke. Malignant peripheral nerve sheath tumors of the oral and maxillofacial region: report of a case and review of the literature[J]. China J Oral Maxillofac Surg, 2014, 12(1): 91-94.

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